Journal of Anaesthesiology Clinical Pharmacology

CASE REPORT
Year
: 2013  |  Volume : 29  |  Issue : 3  |  Page : 390--393

Epidermolysis bullosa: Careful monitoring and no touch principle for anesthesia management


Sujit V Saraf, Nishigandha J Mandawade, Sandeep K Gore, Usha D Padhye, Charissa S Pereira 
 Department of Anaesthesiology, Maharashtra Medical Foundation, Joshi and Ratna Hospitals, Pune, Maharashtra, India

Correspondence Address:
Sujit V Saraf
Maharashtra medical foundation, Joshi and Ratna Hospitals, Pune - 411 004, Maharashtra
India

Epidermolysis bullosa (EB) is a rare genetic mechanobullous disorder, with excessive fragility of the skin and mucous membranes. Avoiding mechanical injury to the skin and mucous membranes is essential in the anesthetic management. Shearing forces applied to the skin result in bullae formation, while compressive forces to the skin are tolerated. The challenge is to use monitoring technology without damaging the epithelial surface. Difficult airway, positioning issues, nutritional deficiencies, poor immunity, and carcinogenic potential add to the comorbidities. We managed a child with EB undergoing syndactyly release. Ensuring maximal skin and mucous membrane protection, anesthesia in children with EB can be conducted with few sequelae.


How to cite this article:
Saraf SV, Mandawade NJ, Gore SK, Padhye UD, Pereira CS. Epidermolysis bullosa: Careful monitoring and no touch principle for anesthesia management.J Anaesthesiol Clin Pharmacol 2013;29:390-393


How to cite this URL:
Saraf SV, Mandawade NJ, Gore SK, Padhye UD, Pereira CS. Epidermolysis bullosa: Careful monitoring and no touch principle for anesthesia management. J Anaesthesiol Clin Pharmacol [serial online] 2013 [cited 2020 Aug 4 ];29:390-393
Available from: http://www.joacp.org/article.asp?issn=0970-9185;year=2013;volume=29;issue=3;spage=390;epage=393;aulast=Saraf;type=0